2014 - 2 Issue

Case report

Acute Posterior Multifocal Placoid Pigment Epitheliopathy – Case Report

Alexandr Stěpanov ORCID
Alena Feuermannová – Jan Studnička ORCID – Libor Hejsek ORCID – Marya Burova ORCID – Naďa Jirásková – Pavel Rozsíval ORCID

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Published in Czech and Slovak Ophtalmology: 2014 - 2

Published on website: 22.04.2014

Keywords: acute posterior multifocal placoid pigment epitheliopathy (APMPPE), white dot syndromes, macular edema

Summary

Acute posterior multifocal placoid pigment epitheliopathy (APMPPE) affects individuals between 20 to 30 years of age and ocular manifestations are often preceded by flu-like illness. Symptoms of the disease include acute vision decrease associated with central and paracentral scotoma. Impairment of vision is usually bilateral, but may be asymmetric. We report the case of a man at the age of twenty-one, who was treated for APMPPE. Due to the involvement of the macula, low visual acuity and related immunogenetic predisposition (HLA-B27 positivity) was recommended corticosteroid therapy with a good therapeutic effect.

References

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